7/22/2019 Caso N 252 Genodermatosis

1/18

Absc pbrb nkbjestkacNr. Lrbeaksac JcezbifzNrb.Bejfikab Hfrfz

7/22/2019 Caso N 252 Genodermatosis

2/18

Felfrofnbn batubi y betfafnfetfs

Lfofekec nf 4bcs ace pficfsabsc nfsnf fiebakokfetc

B ics = ofsfs

ifskcefsfrktfobtcsbs feabrb

Lctcsfeskdkiknbn Pcstfrkcrofetf

fe trbx yfxtrfoknbnfsquf sf tcrebemkpfrarokabs

Nfsbrrciicpkacoctcr ecrobi

Prcnuatc nf KK jfstb1= sfobebs jfstbake PFJ

7/22/2019 Caso N 252 Genodermatosis

3/18

tbiib dbhb y pfsc pcr nfdbhc nf ic ecrobipbrb su fnbn

7/22/2019 Caso N 252 Genodermatosis

4/18

LC^CNFTOB^CQKQ

7/22/2019 Caso N 252 Genodermatosis

5/18

2. Pckqukicnfrokb fe brfbs fxpufstbs4. Obauibs abl ace ifamf fe trbx

1. Mkpfrtficrksoc

7/22/2019 Caso N 252 Genodermatosis

6/18

Oauibs abl ace ifamf

7/22/2019 Caso N 252 Genodermatosis

7/18

Abodkcs pckqukicnfrokacs fe brfbs fxpufstbs

7/22/2019 Caso N 252 Genodermatosis

8/18

Lctcsfeskdkiknbn

7/22/2019 Caso N 252 Genodermatosis

9/18

7/22/2019 Caso N 252 Genodermatosis

10/18

Nfrobtktks fe obecs , pkfs y pikfjufs

7/22/2019 Caso N 252 Genodermatosis

11/18

Ibdcrbtcrkc

Befokb okarcatkab ecrocarokab

Fifvbake nf trbesbokebsbs

Mkpfracopifofetfokb

Pfrlki jbstrcafibac8 ecrobi

Fifatrciktcs fe suncr8 ecrobi

Qfrcicjbs vkrbifs8 efjbtkvbs

akncs crjekacs8 Prcjiutokac y jikarkac (fifvbncs)

Fstunkc keoueclfectkpc8 ecrobi

Pbrbaiekacs

7/22/2019 Caso N 252 Genodermatosis

12/18

Fstunkc jfetkac (> (ec aceaiuyfetf) Fvbiubake nf pcrlkrkebs8 ecrobi

Qoktm Ifoik Cpktz8 efjbtkvc

Qurvfy sfc

Acenrcnkspibskb oftblkskbrkb oitkpif (fnbn sfb ; ofsfs)

Dkcpskb nf pkfi

Fpktfikc bnfijbzbnc y rfatklkabnc, aufrpcs nf akvbtf

Ofibelbjcs y pkjofetc ofiekac ikdrf fe nfrokssupfrlkabi, nfroks lkdrcsb y ibxb

Kelkitrbnc kelibobtcrkc pfrkvbsauibr ikelcmkstkcaktbrkc fsabsc

Felfrofnbn batubi y betfafnfetfs

7/22/2019 Caso N 252 Genodermatosis

13/18

LctcsfeskdkiknbnPckqukicnfrokb acejektbTftbrnc nfi arfakokfetcOauibs Abl ace Ifamf Jfefrbikzbnbs

NfrobtktksFvbiubake Cltbiocijkab NIEFvbiubake Efurcijkab Ecrobi

Mbiibzjcs aiekacs

7/22/2019 Caso N 252 Genodermatosis

14/18

QENTCOF NF TC^OVEN ^MCOPQCENKQRVFTB^CQKQ ACEJFEK^B

BEFOKB NF LBEACEKQENTCOF NF DICCO

PTC^CPCTLKTKB FTK^TCPC[^KAB^TKAC^KCNKQ^TCLKB

Pibetfbokfetcs nkbjestkacs

7/22/2019 Caso N 252 Genodermatosis

15/18

FELFTOFN N AV^ EFC^T Q

O EKLFQ^ AKCEFQECTO IKN N AFIVI T^KPC OFA EKQOC

Pcrlkrkb Lctcsfeskdkiknbnpkfi/chcs

Crkeb rchb

Befokb

Fspifecofjbikb

Nkso. LfrrcqufibtbsbBit. dkcsetfsks

jrupc mfoc

NksqufrbtcsksMkpfrpkjofetbake

Nkstrclkb uejfbi

Ifuacpibqukb

Nkslueake nf onuib sfbNkslea. ficofrbsb

(BEN rkdcscobi)

Outbake jfe

NGA2

^rkactkcnkstrclkb Lctcsfeskdkiknbn. TO. Oufrtf afiuibr pcr V\. Tfpbrbakebecrobi nf BNE.

Qenrcof nfDicco

^fibejkfatbskb.

Lctcsfeskdkiknbn.

Nflfatc nf keoueknbn,

ifuafokb, efcpibskbs JK.

Tcopkokfetc

fspetbefc nfarcocscobs.

BNE mfikabsb

becrobi.

efokb nfLbeacek Mkpfrpkjofetbake. Befokb, pbeaktcpfekb,efcpibskbs mfptkabs.Tcopkokfetc

fspetbefc nf

arcocscobs c pcr

nkfpcxydutbec.

Tfpbrbake

becrobi nfi

fetrfaruzbokfetc

nfi BNE

Jfecnfrobtcsks y lctcsfeskdkiknbn

7/22/2019 Caso N 252 Genodermatosis

16/18

Qenrcof nf Tctmouen-^mcosceMfrfeakb butcsokab rfafskvb

Nfsarktb pcr Tctmouen fe 2=7 :4

7/22/2019 Caso N 252 Genodermatosis

17/18

Obeklfstbakcefs fxtrbautefbsNkspibskb fsqufitkabDbhb fstbturbMkpcjcebnksoc prkobrkc

^rbstcrecs nfetbifs8 Tftbrnc fe frupake nfetbi,

nkfetfs supfreuofrbrkcs, buofetc nf abrkfs, rbkafs

acrtbs.

Lueake keouecijkab f ketfikjfeakb ecrobifs

Tkfsjc nf cstfcsbracob

Crbi Qurjfry, Crbi Ofnkakef, Crbi Pbtmcicjy, Crbi Tbnkcicjy ben Fencncetcicjy 40047;>(>)8>:;->=>

Crbi Qur fr , Crbi Ofnkakef, Crbi Pbtmcic , Crbi Tbnkcic ben Fencncetcic 400:7 20 (2)82 -f44

7/22/2019 Caso N 252 Genodermatosis

18/18

Aubi fs su Nkbjestkac